bs-42132P-APC

DATASHEET

Entrez Gene: 11430

Swiss Prot: Q9R0H0

Source: Recombinant mouse ACOX1 protein is expressed in E.coli with C-His. It contains the amino acid sequence of 386-661/661

Storage Buffer: Aqueous buffered solution containing 0.01M TBS (pH7.4) with 1% BSA, 0.02% Proclin300 and 50% Glycerol.

Storage: Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.

Background:

Defects in ACOX1 are the cause of adrenoleukodystrophy pseudoneonatal (Pseudo-NALD); also known as peroxisomal acyl-CoA oxidase deficiency. Pseudo-NALD is a peroxisomal single-enzyme disorder. Clinical features include mental retardation, leukodystrophy, seizures, mild hepatomegaly, hearing deficit. Pseudo-NALD is characterized by increased plasma levels of very-long chain fatty cids, due to decreased or absent peroxisome acyl-CoA oxidase activity. Peroxisomes are intact and functioning.

Conjugation: APC

Excitation/ Emission: 650nm/660nm

Size: 100ug,500ug

Applications: Others()

Mol. Wt.: 31.8

Species: Others

For research use only. Not intended for diagnostic or therapeutic use.